E75.241ICD-10-CM 2027 · Abrechenbar
Niemann-Pick disease type B
Geschwistercodes
Inclusion terms
- Acid sphingomyelinase deficiency type B (ASMD type B)
- Chronic visceral acid sphingomyelinase deficiency
Vererbt von E75.24: Niemann-Pick disease
Inclusion terms
- Acid sphingomyelinase deficiency (ASMD)
Vererbt von E75.2: Other sphingolipidosis
Excludes1
- adrenoleukodystrophy [Addison-Schilder] (
E71.528)
Vererbt von E75: Disorders of sphingolipid metabolism and other lipid storage disorders
Excludes1
Teil von: E75.24: Niemann-Pick disease › E75.2: Other sphingolipidosis › E75: Disorders of sphingolipid metabolism and other lipid storage disorders