D81.810ICD-10-CM 2027 · Billable
Biotinidase deficiency
Sibling codes
Inherited from D81.81: Biotin-dependent carboxylase deficiency
Excludes1
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (
E53.8)
Inclusion terms
- Multiple carboxylase deficiency
Inherited from D81: Combined immunodeficiencies
Excludes1
- autosomal recessive agammaglobulinemia (Swiss type) (
D80.0)
Part of: D81.81: Biotin-dependent carboxylase deficiency › D81.8: Other combined immunodeficiencies › D81: Combined immunodeficiencies