E88.01ICD-10-CM 2027 · Billable
Alpha-1-antitrypsin deficiency
Sibling codes
Inclusion terms
- AAT deficiency
Inherited from E88.0: Disorders of plasma-protein metabolism, not elsewhere classified
Excludes1
Excludes2
- disorder of lipoprotein metabolism (
E78.-)
Inherited from E88: Other and unspecified metabolic disorders
Excludes1
- histiocytosis X (chronic) (
C96.6)
Use additional code
- codes for associated conditions
Part of: E88.0: Disorders of plasma-protein metabolism, not elsewhere classified › E88: Other and unspecified metabolic disorders