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J84.89

ICD-10-CM 2027 · Billable

Other specified interstitial pulmonary diseases

Sibling codes

  • J84.81 – Lymphangioleiomyomatosis
  • J84.82 – Adult pulmonary Langerhans cell histiocytosis
  • J84.83 – Surfactant mutations of the lung
  • J84.84 – Other interstitial lung diseases of childhood

Code first

  • if applicable: poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
  • underlying cause of pneumonopathy, if known

Excludes1

  • cryptogenic organizing pneumonia (J84.116)
  • idiopathic non-specific interstitial pneumonitis (J84.113)
  • lipoid pneumonia, exogenous or unspecified (J69.1)
  • lymphoid interstitial pneumonia (J84.2)

Inclusion terms

  • Endogenous lipoid pneumonia
  • Interstitial pneumonitis
  • Non-specific interstitial pneumonitis NOS
  • Organizing pneumonia NOS

Use additional code

  • code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced

Inherited from J84.8: Other specified interstitial pulmonary diseases

Excludes1

  • exogenous lipoid pneumonia (J69.1)
  • unspecified lipoid pneumonia (J69.1)

Inherited from J84: Other interstitial pulmonary diseases

Code also

  • if applicable, associated condition

Excludes1

  • drug-induced interstitial lung disorders (J70.2-J70.4)
  • interstitial emphysema (J98.2)

Excludes2

  • lung diseases due to external agents (J60-J70)

Part of: J84.8: Other specified interstitial pulmonary diseases › J84: Other interstitial pulmonary diseases