1A60.0

ICD-11 MMS 2026-01

Early congenital syphilis, symptomatic

Description

A disease affecting newborns or children up to 2 years of age, caused by an infection with the gram-negative bacteria Treponema pallidum pallidum in utero. This disease is characterised by premature birth, hepatosplenomegaly, skeletal abnormalities, and bullous skin disease. Transmission is by vertical transmission.

Index terms

  • Early congenital syphilis, symptomatic
  • Mucocutaneous early congenital syphilis
  • Congenital syphilitic mucous patches
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  • Congenital syphilitic condylomata lata
  • Syphilitic pemphigus
  • Early congenital syphilitic osteochondropathy
  • Congenital syphilitic epiphysitis
  • Congenital syphilitic rhinitis
  • Early congenital syphilitic rhinitis
  • Early congenital syphilitic laryngitis
  • Early congenital syphilitic pharyngitis
  • Congenital syphilitic pneumonia
  • early congenital syphilitic pneumonia
  • Congenital syphilitic splenomegaly
  • Congenital syphilitic synovitis
  • early congenital syphilitic synovitis
  • Early congenital syphilitic oculopathy
  • Congenital syphilitic chorioretinitis
  • Congenital syphilitic choroiditis
  • Early congenital visceral syphilis

Exclusions from above levels

  • FA11.2 – Arthropathy following genitourinary infection
  • GC02.1 – Nonspecific and nongonococcal urethritis
  • NE83.1 – Infection arising from device, implant or graft, not elsewhere classified

Sibling codes

  • 1A60.1 – Early congenital syphilis, latent
  • 1A60.2 – Late congenital syphilitic oculopathy
  • 1A60.3 – Late congenital neurosyphilis
  • 1A60.4 – Other late congenital syphilis, symptomatic
  • 1A60.5 – Late congenital syphilis, latent
  • 1A60.Z – Congenital syphilis, unspecified

Foundation entity

Early congenital syphilis, symptomatic – http://id.who.int/icd/entity/395565060

Allowed postcoordination axes

Part of: 1A60: Congenital syphilis › 01: Certain infectious or parasitic diseases