2A01.00

ICD-11 MMS 2026-01

Primary malignant meningioma

Index terms

  • Primary malignant meningioma
  • meningeal sarcoma of unspecified site
  • meningothelial sarcoma of unspecified site
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  • Familial multiple meningioma

Exclusions from above levels

  • 2D50 – Malignant neoplasm metastasis in brain
  • 2D51 – Malignant neoplasm metastasis in meninges
  • 2D52 – Malignant neoplasm metastasis in spinal cord, cranial nerves or paraspinal nerves

Sibling codes

  • 2A01.0Y – Other specified meningiomas
  • 2A01.0Z – Meningiomas, unspecified

Foundation entity

Primary malignant meningioma – http://id.who.int/icd/entity/1478862889

Allowed postcoordination axes

Part of: 2A01.0: Meningiomas › 2A01: Primary neoplasms of meninges › 02: Neoplasms