2A33

ICD-11 MMS 2026-01

Refractory anaemia with ring sideroblasts

Description

A myelodysplastic syndrome characterised by an anaemia in which 15% or more of the erythroid precursors are ringed sideroblasts. The ring sideroblast is an erythroid precursor in which one third or more of the nucleus is encircled by granules which are positive for iron stain.

Index terms

  • Refractory anaemia with ring sideroblasts
  • RARS - [refractory anaemia with ringed sideroblasts]
  • acquired idiopathic sideroblastic anaemia
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  • primary acquired sideroblastic anaemia
  • refractory anaemia with sideroblasts
  • refractory sideroblastic anaemia
  • Refractory anaemia with hemochromatosis

Exclusions from above levels

  • 2A60.2 – Therapy-related myeloid neoplasms
  • 3A70.10 – Drug-induced aplastic anaemia
  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
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  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A30 – Refractory anaemia
  • 2A31 – Refractory neutropaenia
  • 2A32 – Refractory thrombocytopenia
  • 2A34 – Refractory cytopenia with multi-lineage dysplasia
  • 2A35 – Refractory anaemia with excess of blasts
  • 2A36 – Myelodysplastic syndrome with isolated del(5q)
  • 2A37 – Myelodysplastic syndrome, unclassifiable
  • 2A38 – Refractory cytopenia of childhood
  • 2A3Y – Other specified myelodysplastic syndromes
  • 2A3Z – Myelodysplastic syndromes, unspecified

Foundation entity

Refractory anaemia with ring sideroblasts – http://id.who.int/icd/entity/1793160341

Allowed postcoordination axes

Part of: 02: Neoplasms