2B01

ICD-11 MMS 2026-01

Mycosis fungoides

Description

A peripheral (mature) T-cell lymphoma presenting in the skin with patches/plaques or less commonly with tumours or erythroderma. It is characterised by epidermal and dermal infiltration of small to medium-sized T-cells with cerebriform nuclei.

Index terms

  • Mycosis fungoides
  • Mycosis fungoides with limited patches or plaques
  • Mycosis fungoides stage T1
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  • Mycosis fungoides with extensive patches or plaques
  • Mycosis fungoides stage T2
  • Patch or plaque stage mycosis fungoides
  • Mycosis fungoides, tumour stage
  • T3 stage mycosis fungoides
  • Tumour stage mycosis fungoides
  • Mycosis fungoides, erythrodermic
  • T4 stage mycosis fungoides
  • Mycosis fungoides variants
  • Folliculotropic mycosis fungoides
  • Syringotropic mycosis fungoides
  • syringotropic cutaneous T-cell lymphoma
  • Pagetoid reticulosis
  • Woringer-Kolopp disease
  • Granulomatous slack skin
  • Poikilodermatous mycosis fungoides

Inclusions

  • Folliculotropic mycosis fungoides
  • Pagetoid reticulosis
  • Granulomatous slack skin

Exclusions from above levels

  • 2E08 – Skin infiltration by nodal or non-cutaneous extranodal lymphoma
  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
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  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B00 – Subcutaneous panniculitis-like T-cell lymphoma
  • 2B02 – Sézary syndrome
  • 2B03 – Primary cutaneous CD30-positive T-cell lymphoproliferative disorders
  • 2B0Y – Other specified primary cutaneous mature T-cell or NK-cell lymphomas and lymphoproliferative disorders
  • 2B0Z – Primary cutaneous T-cell lymphoma of undetermined or unspecified type

Foundation entity

Mycosis fungoides – http://id.who.int/icd/entity/901411509

Allowed postcoordination axes

Part of: 02: Neoplasms