2B52.3ICD-11 MMS 2026-01
Ewing sarcoma of soft tissue
Description
A rare malignant neoplasm of the soft tissues. It is typically a disease of children and young adults. It is characterised by t(11:22) (q24: q12) resulting in the expression of EWS/FLI-1 chimeric transcript. Most commonly occurs in the paravertebral region, chest wall, pelvis and lower extremities.
Coding note from above levels
For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.
Index terms
- Ewing sarcoma of soft tissue
- Malignant peripheral neuroectodermal tumour of cervix uteri
Exclusions from above levels
2A01.1– Mesenchymal tumour of meninges2A02.1– Tumours of cranial or paraspinal nerves- http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
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- http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues
Sibling codes
2B52.0– Ewing sarcoma of bone or articular cartilage of limbs2B52.1– Ewing sarcoma of bone or articular cartilage of pelvis2B52.2– Ewing sarcoma of bone or articular cartilage of ribs2B52.Y– Ewing sarcoma of bone or articular cartilage of other specified sites2B52.Z– Ewing sarcoma of bone or articular cartilage of unspecified sites
Foundation entity
Ewing sarcoma of soft tissue – http://id.who.int/icd/entity/1650581103