2C33

ICD-11 MMS 2026-01

Adnexal carcinoma of skin

Description

A carcinoma arising from the sebaceous glands, sweat glands, or the hair follicles. Representative examples include sebaceous carcinoma, apocrine carcinoma, eccrine carcinoma, and pilomatrical carcinoma.

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Index terms

  • Adnexal carcinoma of skin
  • Appendageal carcinoma of skin
  • Malignant neoplasm of skin appendage
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  • Microcystic adnexal carcinoma
  • Primary cutaneous adenoid cystic carcinoma
  • Primary cutaneous mucinous carcinoma
  • Spiradenocarcinoma
  • Tubular carcinoma of the skin
  • malignant spiradenoma
  • Sebaceous carcinoma of eyelid
  • Aggressive digital papillary adenocarcinoma
  • Apocrine carcinoma
  • Hidradenocarcinoma
  • Porocarcinoma of sweat glands
  • malignant chondroid syringoma
  • malignant clear-cell hidradenoma
  • malignant eccrine poroma
  • malignant neoplasm of sweat glands
  • sclerosing sweat duct carcinoma
  • sweat gland carcinoma
  • Malignant neoplasm of sebaceous glands
  • Sebaceous carcinoma of skin

Inclusions

  • Appendageal carcinoma of skin
  • Primary cutaneous adenoid cystic carcinoma
  • Primary cutaneous mucinous carcinoma

Exclusions from above levels

  • 2E08 – Malignant neoplasm metastasis in skin
  • 2E64 – Carcinoma in situ of skin
  • http://id.who.int/icd/entity/1965082709 – Malignant mesenchymal neoplasms
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  • http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
  • http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Sibling codes

  • 2C30 – Melanoma of skin
  • 2C31 – Squamous cell carcinoma of skin
  • 2C32 – Basal cell carcinoma of skin
  • 2C34 – Cutaneous neuroendocrine carcinoma
  • 2C35 – Cutaneous sarcoma
  • 2C3Y – Other specified malignant neoplasms of skin
  • 2C3Z – Malignant neoplasm of skin of unknown or unspecified type

Foundation entity

Adnexal carcinoma of skin – http://id.who.int/icd/entity/712393740

Allowed postcoordination axes

Part of: 02: Neoplasms