2C40

ICD-11 MMS 2026-01

Malignant neuroepitheliomatous neoplasms of peripheral nerves or autonomic nervous system

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Index terms

  • Malignant neuroepitheliomatous neoplasms of peripheral nerves or autonomic nervous system
  • PNE - [peripheral neuroepithelioma]
  • peripheral neuroepithelioma

Exclusions from above levels

  • 2B5E – Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
  • http://id.who.int/icd/entity/1965082709 – Malignant mesenchymal neoplasms
  • http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
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  • http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Sibling codes

  • 2C41 – Malignant perineurioma
  • 2C4Y – Other specified malignant neoplasms of peripheral nerves or autonomic nervous system
  • 2C4Z – Malignant neoplasms of peripheral nerves or autonomic nervous system, unspecified

Foundation entity

Malignant neuroepitheliomatous neoplasms of peripheral nerves or autonomic nervous system – http://id.who.int/icd/entity/355612100

Allowed postcoordination axes

Part of: 02: Neoplasms