2C90.0

ICD-11 MMS 2026-01

Renal cell carcinoma of kidney, except renal pelvis

Description

There is a strong correlation between cigarette smoking and the development of renal cell carcinoma. The clinical presentation includes: haematuria, flank pain and a palpable lumbar mass. A high percentage of renal cell carcinomas are diagnosed when an ultrasound is performed for other purposes. Diagnostic procedures include: ultrasound, intravenous pyelography and computerised tomography (CT).

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Index terms

  • Renal cell carcinoma of kidney, except renal pelvis
  • hypernephroma NOS
  • hypernephroma of kidney
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  • nephroma of kidney
  • renal cell adenocarcinoma of kidney
  • renal cell carcinoma NOS
  • renal cell carcinoma unspecified site
  • Renal cystic neoplasms, cystic renal cell carcinoma
  • Collecting duct carcinoma
  • bellini duct carcinoma
  • SMARCB1 deficient renal medullary carcinoma
  • SMARCB1 [SWI/SNF-related, matrix-associated, actin-dependent regulator of chromatin, subfamily B, member 1] deficient renal medullary carcinoma
  • renal medullary carcinoma
  • Familial renal cell carcinoma
  • Hereditary leiomyomatosis and renal cell cancer
  • Familial leiomyomatosis cutis et uteri
  • HLRCC - [hereditary leiomyomatosis and renal cell cancer]
  • Hereditary multiple cutaneous leiomyomas
  • Multiple cutaneous or uterine leiomyomata 1, with or without renal cell carcinoma
  • Reed syndrome
  • Familial papillary renal cell carcinoma

Exclusions from above levels

  • 2C91 – Malignant neoplasm of renal calyces
  • 2E00 – Malignant neoplasm metastasis in kidney or renal pelvis
  • http://id.who.int/icd/entity/1965082709 – Malignant mesenchymal neoplasms
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  • http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
  • http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Sibling codes

  • 2C90.Y – Other specified malignant neoplasms of kidney, except renal pelvis
  • 2C90.Z – Malignant neoplasms of kidney, except renal pelvis, unspecified

Foundation entity

Renal cell carcinoma of kidney, except renal pelvis – http://id.who.int/icd/entity/825917541

Allowed postcoordination axes

Part of: 2C90: Malignant neoplasms of kidney, except renal pelvis › 02: Neoplasms