2D02.2

ICD-11 MMS 2026-01

Retinoblastoma

Description

Retinoblastoma is the most common intraocular malignancy in children. It is a life threatening condition but is potentially curable. It can be hereditary or non-hereditary, unilateral or bilateral (unilateral retinoblastoma, bilateral retinoblastoma, see these terms).

Coding note from above levels

For use of this category, reference should be made to the mortality coding rules and guidelines in the Reference Guide.

Index terms

  • Retinoblastoma
  • Differentiated retinoblastoma
  • Undifferentiated retinoblastoma

Exclusions from above levels

  • http://id.who.int/icd/entity/1965082709 – Malignant mesenchymal neoplasms
  • 2A02 – Malignant neoplasm of optic nerve
  • http://id.who.int/icd/entity/1706880799 – Malignant neoplasm of skin of eyelid
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  • http://id.who.int/icd/entity/879154182 – Neoplasms of central nervous system or related structures
  • http://id.who.int/icd/entity/944754984 – Neoplasms of haematopoietic or lymphoid tissues

Sibling codes

  • 2D02.0 – Adenocarcinoma of retinal pigment epithelium
  • 2D02.1 – Malignant neuroepithelial tumours of retina
  • 2D02.Y – Other specified malignant neoplasm of retina
  • 2D02.Z – Malignant neoplasm of retina, unspecified

Foundation entity

Retinoblastoma – http://id.who.int/icd/entity/1855353671

Allowed postcoordination axes

Part of: 2D02: Malignant neoplasm of retina › 02: Neoplasms