2E64.1ICD-11 MMS 2026-01
Extramammary Paget disease of skin
Description
An intraepithelial adenocarcinoma of apocrine gland-bearing skin and mucous membrane. Clinically it presents as sharply demarcated erythematous plaques most commonly affecting the vulva in women and perianal skin in men.
Index terms
- Extramammary Paget disease of skin
- EMPD - [extramammary Paget disease]
- Extramammary Paget disease of penis
Show allHide
- Extramammary Paget disease of anus
- Extramammary Paget disease of anogenital skin
Exclusions from above levels
2E63– Melanoma in situ neoplasms
Foundation children elsewhere
2E67.11– Vulvar Paget disease
Sibling codes
Foundation entity
Extramammary Paget disease of skin – http://id.who.int/icd/entity/1796624917