Paget disease of nipple

Description

Paget disease of the nipple describes a rare presentation of breast cancer, seen most frequently in women aged 50-60, manifesting with nipple drainage and itching, erythema, crusty, excoriated nipple, thickened plaques and hyperpigmentation (less frequently). It is due to tumour cells invading the nipple-areola complex and represents 1%-3% of all new breast cancer diagnoses.

Index terms

Paget disease of nipple

Exclusions from above levels

2E63 – melanoma in situ of breast (skin)
2E64 – carcinoma in situ of skin of breast

Sibling codes

2E65.0 – Lobular carcinoma in situ of breast
2E65.1 – Lobular carcinoma in situ of breast, pleomorphic subtype
2E65.2 – Ductal carcinoma in situ of breast
2E65.3 – Ductal carcinoma in situ of breast, comedo subtype
2E65.4 – Mixed ductal and lobular carcinoma in situ of breast
2E65.Y – Other specified carcinoma in situ of breast
2E65.Z – Carcinoma in situ of breast, unspecified

Foundation entity

Paget disease of nipple – http://id.who.int/icd/entity/1295910447

Allowed postcoordination axes

Part of: 2E65: Carcinoma in situ of breast › 02: Neoplasms