2F20.2

ICD-11 MMS 2026-01

Congenital melanocytic naevus

Description

Congenital melanocytic naevi are circumscribed areas of skin pigmentation present at birth as a result of abnormal intrauterine proliferation of melanocytes within the dermis, the epidermis or both. They may range in size from a few millimetres to many centimetres in diameter. If their projected or final adult maximal diameter is greater than 20 cm they are termed giant congenital melanocytic naevi.

Child codes

  • 2F20.20 – Giant congenital melanocytic naevus
  • 2F20.2Y – Other specified congenital melanocytic naevus
  • 2F20.2Z – Congenital melanocytic naevus, unspecified

Sibling codes

  • 2F20.0 – Common acquired melanocytic naevus
  • 2F20.1 – Atypical melanocytic naevus
  • 2F20.3 – Generalised eruptive melanocytic naevi
  • 2F20.Y – Other specific types of melanocytic naevus
  • 2F20.Z – Melanocytic naevus, unspecified

Foundation entity

Congenital melanocytic naevus – http://id.who.int/icd/entity/887489797

Allowed postcoordination axes

Part of: 2F20: Benign cutaneous melanocytic neoplasms › 02: Neoplasms