5A44

ICD-11 MMS 2026-01

Insulin-resistance syndromes

Index terms

  • Insulin-resistance syndromes
  • Insulin-resistance syndrome type A
  • Insulin-resistance syndrome type B
Show allHide
  • Rabson-Mendenhall syndrome
  • Laminopathy type Decaudain-Vigouroux
  • Laminopathy with severe metabolic syndrome and myopathy
  • Leprechaunism
  • Donohue syndrome
  • HAIR-AN syndrome
  • HAIR-AN - [hyperandrogenic-insulin resistance-acanthosis nigricans] syndrome
  • Insulin resistance - short fifth metacarpals
  • Berardinelli-Seip congenital lipodystrophy
  • BSCL - [Berardinelli-Seip congenital lipodystrophy]
  • Berardinelli type lipodystrophy
  • Berardinelli-Seip syndrome
  • Brunzell syndrome
  • Lipoatrophic diabetes
  • Familial partial lipodystrophy
  • Hereditary partial lipodystrophy
  • Familial partial lipodystrophy, Köbberling type
  • FPLD1 - [Familial partial lipodystrophy type 1]
  • Familial partial lipodystrophy type 1
  • Familial partial lipodystrophy, Dunnigan type
  • Dunnigan syndrome
  • FPLD2 - [Familial partial lipodystrophy type 2]
  • Familial partial lipodystrophy type 2
  • Familial partial lipodystrophy associated with PPARG mutations
  • FPLD3 - [Familial partial lipodystrophy type 3]
  • Familial partial lipodystrophy type 3
  • Familial partial lipodystrophy due to AKT2 mutations
  • Familial partial lipodystrophy due to lamin-A mutations
  • Severe lipodystrophic laminopathy
  • Familial partial lipodystrophy associated with PLIN1 mutations
  • Acquired generalised lipodystrophy
  • Metabolic syndrome
  • metabolic syndrome NOS

Exclusions from above levels

  • 2C10 – Malignant neoplasm of pancreas
  • 2E92.9 – Benign neoplasm of endocrine pancreas
  • 2F7A.0 – Multiple endocrine neoplasia type 1
Show allHide
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5A40 – Intermediate hyperglycaemia
  • 5A41 – Hypoglycaemia without associated diabetes
  • 5A42 – Increased secretion of glucagon
  • 5A43 – Abnormal secretion of gastrin
  • 5A45 – Persistent hyperinsulinaemic hypoglycaemia of infancy
  • 5A4Y – Other specified disorders of glucose regulation or pancreatic internal secretion
  • 5A4Z – Disorders of glucose regulation or pancreatic internal secretion, unspecified

Foundation entity

Insulin-resistance syndromes – http://id.who.int/icd/entity/1736778

Allowed postcoordination axes

Part of: 05: Endocrine, nutritional or metabolic diseases