5A73

ICD-11 MMS 2026-01

Hypoaldosteronism

Index terms

  • Hypoaldosteronism
  • Familial hypoaldosteronism
  • Aldosterone synthase deficiency
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  • Hereditary hypoaldosteronism
  • Familial hyperreninaemic hypoaldosteronism type 1
  • CMO - [Corticosterone methyl-oxidase] deficiency
  • Corticosterone methyl-oxidase deficiency
  • FHHA1 - [Familial hyperreninaemic hypoaldosteronism type 1]
  • Hereditary hyperreninaemic hypoaldosteronism type 1
  • Familial hyperreninaemic hypoaldosteronism type 1A
  • Familial hyperreninaemic hypoaldosteronism type 1A [FHHA1A, 18-hydroxylase deficiency]
  • Familial hyperreninaemic hypoaldosteronism type 1B
  • Familial hyperreninaemic hypoaldosteronism type 1B [FHHA1B, 18-oxidase deficiency]
  • Familial hyperreninaemic hypoaldosteronism type 2
  • FHHA2 - [Familial hyperreninaemic hypoaldosteronism type 2]
  • Hereditary hyperreninaemic hypoaldosteronism type 2

Excludes

  • 5A71.01 – Congenital adrenal hyperplasia

Exclusions from above levels

  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5A70 – Cushing syndrome
  • 5A71 – Adrenogenital disorders
  • 5A72 – Hyperaldosteronism
  • 5A74 – Adrenocortical insufficiency
  • 5A75 – Adrenomedullary hyperfunction
  • 5A76 – Certain specified disorders of adrenal gland
  • 5A7Z – Disorders of the adrenal glands or adrenal hormone system, unspecified

Foundation entity

Hypoaldosteronism – http://id.who.int/icd/entity/1600625317

Part of: 05: Endocrine, nutritional or metabolic diseases