EA93ICD-11 MMS 2026-01
Pityriasis lichenoides
Description
Pityriasis lichenoides is an uncommon inflammatory skin disease of unknown aetiology. It can range from a relatively mild chronic form to a fulminant form with skin necrosis and severe constitutional symptoms. The disease can last from just weeks to months or years. The chronic form is manifest as multiple small flat asymptomatic scaly papules located predominantly on the trunk and proximal limbs. The acute forms present with the abrupt appearance of multiple papules in the same distribution which rapidly progress to haemorrhagic blisters and ulceration.
Index terms
- Pityriasis lichenoides
- Pityriasis lichenoides chronica
- Guttate parapsoriasis
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- Parapsoriasis guttata [Brocq]
- Pityriasis lichenoides et varioliformis acuta
- Mucha-Habermann disease
- PLEVA - [Pityriasis lichenoides et varioliformis acuta]
- Pityriasis lichenoides acuta
- Febrile ulceronecrotic Mucha-Habermann disease
- FUNMH - [Febrile ulceronecrotic Mucha-Habermann disease]
Inclusions
- Pityriasis lichenoides chronica
- Pityriasis lichenoides et varioliformis acuta
- Febrile ulceronecrotic Mucha-Habermann disease
Exclusions from above levels
1B72.0– Bullous impetigo of the napkin area1F23.12– Napkin candidosisEH71– Dermatoses precipitated by drug therapy
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EH76– Dermatoses associated with specific classes of medication
Sibling codes
Foundation entity
Pityriasis lichenoides – http://id.who.int/icd/entity/266281219
Part of: 14: Diseases of the skin