EA93

ICD-11 MMS 2026-01

Pityriasis lichenoides

Description

Pityriasis lichenoides is an uncommon inflammatory skin disease of unknown aetiology. It can range from a relatively mild chronic form to a fulminant form with skin necrosis and severe constitutional symptoms. The disease can last from just weeks to months or years. The chronic form is manifest as multiple small flat asymptomatic scaly papules located predominantly on the trunk and proximal limbs. The acute forms present with the abrupt appearance of multiple papules in the same distribution which rapidly progress to haemorrhagic blisters and ulceration.

Index terms

  • Pityriasis lichenoides
  • Pityriasis lichenoides chronica
  • Guttate parapsoriasis
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  • Parapsoriasis guttata [Brocq]
  • Pityriasis lichenoides et varioliformis acuta
  • Mucha-Habermann disease
  • PLEVA - [Pityriasis lichenoides et varioliformis acuta]
  • Pityriasis lichenoides acuta
  • Febrile ulceronecrotic Mucha-Habermann disease
  • FUNMH - [Febrile ulceronecrotic Mucha-Habermann disease]

Inclusions

  • Pityriasis lichenoides chronica
  • Pityriasis lichenoides et varioliformis acuta
  • Febrile ulceronecrotic Mucha-Habermann disease

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EA90 – Psoriasis
  • EA91 – Lichen planus
  • EA92 – Lichenoid dermatoses
  • EA94 – Pityriasis rubra pilaris
  • EA95 – Small plaque parapsoriasis

Foundation entity

Pityriasis lichenoides – http://id.who.int/icd/entity/266281219

Part of: 14: Diseases of the skin