EB41.0

ICD-11 MMS 2026-01

Bullous pemphigoid

Description

Bullous pemphigoid is the most common autoimmune blistering disease in the Western world. It chiefly affects the elderly and typically presents with a pruritic urticated erythema which evolves into a widespread eruption of intact tense blisters. It can sometimes involve mucous membranes. It is characterised by IgG antibodies to the basement membrane zone, leading to subepidermal clefts that are clinically manifest as blisters.

Index terms

  • Bullous pemphigoid

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB41.1 – Mucous membrane pemphigoid
  • EB41.Y – Other specified pemphigoid
  • EB41.Z – Pemphigoid, unspecified

Foundation entity

Bullous pemphigoid – http://id.who.int/icd/entity/233308710

Part of: EB41: Pemphigoid › 14: Diseases of the skin