EB60.0

ICD-11 MMS 2026-01

Lichen sclerosus of vulva

Description

Lichen sclerosus of the vulva is an inflammatory disorder of unknown aetiology affecting the skin of the vulva and perianal area. Typically it affects women in the fifth and sixth decades of life though is not uncommon in prepubertal girls. It presents with pruritus, soreness or dyspareunia. The affected skin is white and atrophic, though secondary changes including maceration, purpura and erosion may dominate the clinical picture. In longstanding cases there may be marked shrinkage of the vulva, labial fusion and an increased risk of malignant transformation.

Index terms

  • Lichen sclerosus of vulva
  • Kraurosis vulvae
  • Lichen sclerosus et atrophicus of vulva
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  • Vulval lichen sclerosus
  • Prepubertal vulval lichen sclerosus
  • Lichen sclerosus of vulva, prepubertal

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB60.1 – Lichen sclerosus of penis
  • EB60.Y – Lichen sclerosus of other specified sites
  • EB60.Z – Lichen sclerosus, unspecified

Foundation entity

Lichen sclerosus of vulva – http://id.who.int/icd/entity/1601273294

Part of: EB60: Lichen sclerosus › 14: Diseases of the skin