EB61.1

ICD-11 MMS 2026-01

Linear morphoea

Description

Linear morphoea is a form of morphoea which usually presents in childhood or adolescence and is usually unilateral, affecting a limb with a linear induration of skin, subcutis and occasionally underlying muscle and bone. It may also affect the scalp and forehead ("en coup de sabre") producing a depressed scar likened to a healed sabre wound, with sclerosis of the skin and alopecia of affected scalp.

Index terms

  • Linear morphoea
  • Linear scleroderma
  • Morphoea en coup de sabre

Exclusions from above levels

  • 1B72.0 – Bullous impetigo of the napkin area
  • 1F23.12 – Napkin candidosis
  • EH71 – Dermatoses precipitated by drug therapy
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  • EH76 – Dermatoses associated with specific classes of medication

Sibling codes

  • EB61.0 – Plaque morphoea
  • EB61.Y – Other specified forms of morphoea
  • EB61.Z – Morphoea, unspecified

Foundation entity

Linear morphoea – http://id.who.int/icd/entity/806129669

Part of: EB61: Morphoea › 14: Diseases of the skin