EC22.0

ICD-11 MMS 2026-01

Inherited deformities of nails

Description

Genetically-determined abnormalities of nail development.

Index terms

  • Inherited deformities of nails
  • Hereditary koilonychia
  • NDNC2 - [nail disorder, nonsyndromic, congenital 2] (MIM 149300)
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  • Spoon nails (inherited)
  • congenital koilonychia
  • Hereditary trachyonychia
  • NDNC1 - [nail disorder, nonsyndromic, congenital 1] (MIM161050)
  • Twenty nail dystrophy
  • Hereditary distal onycholysis
  • NDNC5 - [nail disorder, nonsyndromic, congenital 5] (MIM 164800)
  • Partial onycholysis with scleronychia
  • Hereditary brachyonychia
  • Racquet nails
  • Hereditary onychodysplasia
  • Isolated congenital onychodysplasia
  • NDNC7 - [nail disorder, nonsyndromic, congenital 7] (MIM 605779)
  • Hereditary leukonychia
  • Congenital leukonychia
  • NDNC3 - [nail disorder, nonsyndromic, congenital 3] (MIM 151600)
  • Porcelain nails
  • True leukonychia
  • Total leukonychia
  • Subtotal leukonychia
  • Other specified isolated inherited deformity of nails
  • Hereditary anonychia
  • Congenital absence of nails
  • Congenital anonychia

Foundation entity

Inherited deformities of nails – http://id.who.int/icd/entity/1688094957

Part of: EC22: Genetic defects of nails or nail growth › 14: Diseases of the skin