ED52

ICD-11 MMS 2026-01

Porokeratoses

Description

Porokeratoses result from a clonal disorder of keratinization. They are characterised by one or more atrophic patches surrounded by a clinically and histologically distinctive ridged hyperkeratotic border (cornoid lamella). Multiple clinical variants of porokeratosis are recognised.

Index terms

  • Porokeratoses
  • Disseminated superficial porokeratosis
  • Disseminated superficial actinic porokeratosis
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  • DSAP - [disseminated superficial actinic porokeratosis]
  • Eruptive disseminated porokeratosis
  • Localised porokeratosis
  • Porokeratosis of Mibelli
  • Giant porokeratosis
  • Linear porokeratosis
  • Genital porokeratosis

Sibling codes

  • ED50 – Ichthyoses
  • ED51 – Diffuse epidermal hyperkeratosis or acanthosis
  • ED53 – Skin peeling
  • ED54 – Xerosis cutis or asteatosis
  • ED55 – Palmoplantar keratodermas
  • ED56 – Keratosis pilaris
  • ED5Y – Other specified disorders of epidermal keratinisation

Foundation entity

Porokeratoses – http://id.who.int/icd/entity/29524620

Part of: 14: Diseases of the skin