EE01.1

ICD-11 MMS 2026-01

Hypohidrosis due to genetic abnormalities of eccrine gland structure or function

Description

Hypohidrosis due to a heritable disorder of sweat gland or duct development. Sweating may be severely diminished or absent due to a paucity or absence of eccrine glands or to defective autonomic innervation. An absence of sweating leads to an inability to thermoregulate by evaporative cooling, and hyperthermia can occur with physical exertion or in a warm environment.

Index terms

  • Hypohidrosis due to genetic abnormalities of eccrine gland structure or function

Foundation children elsewhere

  • 8C21.2 – Hereditary sensory and autonomic neuropathy type IV

Sibling codes

  • EE01.0 – Hypohidrosis attributable to defective sudomotor innervation or function
  • EE01.2 – Hypohidrosis of undetermined aetiology
  • EE01.Y – Other specified forms of hypohidrosis
  • EE01.Z – Hypohidrosis, unspecified

Foundation entity

Hypohidrosis due to genetic abnormalities of eccrine gland structure or function – http://id.who.int/icd/entity/351548110

Allowed postcoordination axes

Part of: EE01: Hypohidrosis › 14: Diseases of the skin