EH40.3

ICD-11 MMS 2026-01

Acute haemorrhagic oedema of infancy

Description

Acute haemorrhagic oedema is an immune complex-mediated cutaneous vasculitis usually associated with respiratory infection or immunization. It affects children between the ages of 4 months and 2 years, with males being affected twice as frequently as females. The dramatic clinical appearance of facial and limb oedema with multiple targetoid purpuric macules belies its generally benign course.

Index terms

  • Acute haemorrhagic oedema of infancy

Exclusions from above levels

  • http://id.who.int/icd/entity/653663824 – Congenital malformations affecting the skin
  • LD27 – Syndromes with skin or mucosal anomalies as a major feature

Sibling codes

  • EH40.0 – Infantile seborrhoeic dermatitis
  • EH40.1 – Infantile napkin dermatoses
  • EH40.2 – Erythrodermas of infancy
  • EH40.Y – Other specified dermatoses of infancy
  • EH40.Z – Dermatoses of infancy, unspecified

Foundation entity

Acute haemorrhagic oedema of infancy – http://id.who.int/icd/entity/1373217935

Part of: EH40: Dermatoses of infancy › 14: Diseases of the skin