LA12.2

ICD-11 MMS 2026-01

Congenital aphakia

Description

Congenital primary aphakia is a developmental eye defect characterised by an absence of the lens, and can be associated with variable secondary ocular defects (including aplasia/dysplasia of the anterior segment of the eye, microphthalmia, and in some cases absence of the iris, retinal dysplasia, or sclerocornea).

Index terms

  • Congenital aphakia
  • agenesis of lens
  • congenital absence of lens
Show allHide
  • Primary aphakia, unilateral
  • Primary aphakia, bilateral

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA12.0 – Coloboma of lens
  • LA12.1 – Congenital cataract
  • LA12.3 – Spherophakia
  • LA12.Y – Other specified structural developmental anomalies of lens or zonula
  • LA12.Z – Structural developmental anomalies of lens or zonula, unspecified

Foundation entity

Congenital aphakia – http://id.who.int/icd/entity/885383581

Allowed postcoordination axes

Part of: LA12: Structural developmental anomalies of lens or zonula › 20: Developmental anomalies