LA31.3

ICD-11 MMS 2026-01

Macrostomia

Description

Congenital macrostomia or transverse facial cleft is a rare congenital craniofacial anomaly. It is usually associated with deformities of other structures developed from the first and second branchial arches and is thought to be part of the manifestations of hemifacial microsomia, the second most common congenital craniofacial anomaly.

Index terms

  • Macrostomia
  • Congenital macrostomia
  • Transverse facial cleft

Inclusions

  • Transverse facial cleft

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA31.0 – Congenital macroglossia
  • LA31.1 – Hypoglossia or aglossia
  • LA31.2 – Ankyloglossia
  • LA31.4 – Microstomia
  • LA31.Y – Other specified structural developmental anomalies of mouth or tongue
  • LA31.Z – Structural developmental anomalies of mouth or tongue, unspecified

Foundation entity

Macrostomia – http://id.who.int/icd/entity/799651914

Part of: LA31: Structural developmental anomalies of mouth or tongue › 20: Developmental anomalies