LA80.3

ICD-11 MMS 2026-01

Extrathoracic heart

Description

A congenital cardiovascular malformation in which the heart is at least partially outside of the thorax.

Index terms

  • Extrathoracic heart
  • Ectopia cordis
  • congenital heart ectopia

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA80.0 – Laevocardia
  • LA80.1 – Dextrocardia
  • LA80.2 – Mesocardia
  • LA80.Y – Other specified anomalous position-orientation of heart
  • LA80.Z – Anomalous position-orientation of heart, unspecified

Foundation entity

Extrathoracic heart – http://id.who.int/icd/entity/285576893

Part of: LA80: Anomalous position-orientation of heart › 20: Developmental anomalies