LA83

ICD-11 MMS 2026-01

Right isomerism

Description

A congenital cardiovascular malformation that is a variant of heterotaxy syndrome in which some paired structures on opposite sides of the left-right axis of the body are symmetrical mirror images of each other, and have the morphology of the normal right-sided structures.

Index terms

  • Right isomerism
  • Asplenia syndrome
  • Splenic agenesis syndrome
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  • bilateral right-sidedness

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA80 – Anomalous position-orientation of heart
  • LA81 – Abnormal ventricular relationships
  • LA82 – Total mirror imagery
  • LA84 – Left isomerism
  • LA85 – Congenital anomaly of an atrioventricular or ventriculo-arterial connection
  • LA86 – Congenital anomaly of mediastinal vein
  • LA87 – Congenital anomaly of an atrioventricular valve or atrioventricular septum
  • LA88 – Congenital anomaly of a ventricle or the ventricular septum
  • LA89 – Functionally univentricular heart
  • LA8A – Congenital anomaly of a ventriculo-arterial valve or adjacent regions
  • LA8B – Congenital anomaly of great arteries including arterial duct
  • LA8C – Congenital anomaly of coronary artery
  • LA8D – Congenital pericardial anomaly
  • LA8E – Congenital anomaly of atrial septum
  • LA8F – Congenital anomaly of right atrium
  • LA8G – Congenital anomaly of left atrium
  • LA8Y – Other specified structural developmental anomaly of heart or great vessels
  • LA8Z – Structural developmental anomaly of heart or great vessels, unspecified

Foundation entity

Right isomerism – http://id.who.int/icd/entity/1576694141

Part of: 20: Developmental anomalies