LA86.3

ICD-11 MMS 2026-01

Congenital pulmonary venous stenosis or hypoplasia

Description

A congenital cardiovascular malformation with a pathologic narrowing of one or more pulmonary veins including diffuse hypoplasia, long segment focal/tubular stenosis and/or discrete stenosis.

Index terms

  • Congenital pulmonary venous stenosis or hypoplasia
  • Congenital hypoplasia of pulmonary vein
  • Congenital pulmonary venous hypoplasia
Show allHide
  • Congenital pulmonary venous stenosis
  • Congenital stenosis of pulmonary vein
  • congenital pulmonary vein stenosis or hypoplasia

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA86.0 – Left superior caval vein
  • LA86.1 – Unroofed coronary sinus
  • LA86.2 – Anomalous pulmonary venous connection
  • LA86.Y – Other specified congenital anomaly of mediastinal vein
  • LA86.Z – Congenital anomaly of mediastinal vein, unspecified

Foundation entity

Congenital pulmonary venous stenosis or hypoplasia – http://id.who.int/icd/entity/469101490

Part of: LA86: Congenital anomaly of mediastinal vein › 20: Developmental anomalies