LA8E.2ICD-11 MMS 2026-01
Sinus venosus defect
Description
A congenital cardiovascular malformation in which there is a caval vein (vena cava) and/or pulmonary vein (or veins) that overrides the atrial septum or the septum secundum (superior interatrial fold) producing an interatrial or anomalous veno-atrial communication. Additional information: although the term sinus venosus atrial septal defect is commonly used, the lesion is more properly termed a sinus venosus communication because, while it functions as an interatrial communication, this lesion is not a defect of the atrial septum.
Index terms
- Sinus venosus defect
- Sinus venosus atrial septal defect
- Sinus venosus communication
Exclusions from above levels
- http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism
Sibling codes
Foundation entity
Sinus venosus defect – http://id.who.int/icd/entity/1930019148
Part of: LA8E: Congenital anomaly of atrial septum › 20: Developmental anomalies