LB01

ICD-11 MMS 2026-01

Omphalocele

Description

Omphalocele is an embryopathy classified in the group of abdominal celosomias and is characterised by a large hernia of the abdominal wall, centred on the umbilical cord, in which the protruding viscera are protected by a sac.

Index terms

  • Omphalocele
  • Exomphalos
  • exumbilication
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  • Epiplosarcomphalocele
  • Sarcoepiplomphalocele
  • Amniocele

Excludes

  • DD53 – Umbilical hernia

Exclusions from above levels

  • LD2F.10 – Prune belly syndrome
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB00 – Structural developmental anomalies of diaphragm
  • LB02 – Gastroschisis
  • LB03 – Structural developmental anomalies of umbilical cord
  • LB0Y – Other specified structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
  • LB0Z – Structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord, unspecified

Foundation entity

Omphalocele – http://id.who.int/icd/entity/1168696429

Part of: 20: Developmental anomalies