LB13.0ICD-11 MMS 2026-01
Congenital hypertrophic pyloric stenosis
Description
A not uncommon congenital malformation of the stomach of unknown cause in which there is hypertrophy and hyperplasia of the circular muscle of the pylorus. Symptoms of gastric outlet obstruction usually appear between the third and sixth weeks of life. The anomaly is manifested by intermittent vomiting (which increases in frequency and becomes projectile), regurgitation, weight loss, dehydration, electrolyte imbalance, sometimes a small palpable pyloric mass, and visible peristaltic contractions across the epigastrium; there may also be jaundice. Some cases appear to be familial (possibly of autosomal dominant inheritance).
Index terms
- Congenital hypertrophic pyloric stenosis
- Congenital or infantile constriction of pylorus
- Congenital or infantile spasm of pylorus
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- achalasia of the pylorus
- congenital constriction of the pylorus
- congenital hypertrophy of the pylorus
- congenital or infantile obstruction of pylorus
- congenital pyloric spasm
- congenital pyloric stenosis
- congenital pyloric stricture
- congenital pylorospasm
- congenital spasm of pylorus
- congenital stenosis of the pylorus
- congenital stricture of the pylorus
- infantile constriction of the pylorus
- infantile hypertrophic pyloric stenosis
- infantile hypertrophy of the pylorus
- infantile pyloric hypertrophy
- infantile pyloric obstruction
- infantile pyloric stenosis
- infantile pyloric stricture
- infantile stenosis of the pylorus
- infantile stricture of the pylorus
- pyloric constriction
- pylorus achalasia
Exclusions from above levels
- http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism
Sibling codes
Foundation entity
Congenital hypertrophic pyloric stenosis – http://id.who.int/icd/entity/224753192
Part of: LB13: Structural developmental anomalies of stomach › 20: Developmental anomalies