LB15.1

ICD-11 MMS 2026-01

Atresia of small intestine

Description

Jejunoileal atresias and stenoses are major causes of neonatal intestinal obstruction. Atresia refers to a congenital obstruction with complete occlusion of the intestinal lumen. It accounts for 95% of obstructions. Four types of jejunoileal atresias are described. They can range from having a small area of blockage or web to missing large sections of the intestines. Intestinal atresia is one of the most frequent causes of bowel obstruction in the newborn. The ileal atresia is more common than jejunal atresia, and multiple foci are more common than isolated atresia. The most accepted theory regarding the etiology of jejunoileal atresia is that of an intrauterine vascular accident resulting in necrosis of the affected segment. Stenosis, on the other hand, refers to a partial occlusion with incomplete obstruction and accounts for the remaining 5% of cases. A stenosis has an intact mesentery and is a localised narrowing of the bowel. No loss of continuity of the lumen exists.

Index terms

  • Atresia of small intestine
  • Congenital absence of small intestine
  • Congenital stenosis of small intestine
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  • congenital small intestinal stricture NOS
  • Multiple-level intestinal atresia
  • Small intestine atresia type IV
  • Congenital absence, atresia or stenosis of jejunum
  • Atresia of jejunum type I
  • Atresia of jejunum type II
  • Atresia of jejunum type IIIa
  • Apple-peel deformity
  • Apple-peel syndrome
  • Christmas tree syndrome
  • Christmas-tree deformity
  • Multiple atresias of jejunum type IV
  • Congenital stenosis of jejunum
  • congenital jejunal stenosis
  • stenosis of jejunum
  • Congenital absence of jejunum
  • jejunal agenesis
  • jejunum agenesis
  • Congenital atresia of jejunum
  • atresia of jejunum
  • jejunal atresia
  • jejunum atresia
  • Congenital imperforate of jejunum
  • Imperforate jejunum
  • jejunal imperforate
  • Congenital stricture of jejunum
  • Congenital absence, atresia or stenosis of ileum
  • Atresia of ileum type I
  • Atresia of ileum type II
  • Atresia of ileum type IIIa
  • Congenital stenosis of ileum
  • congenital ileum obstruction
  • Congenital absence of ileum
  • ileum agenesis
  • Congenital atresia of ileum
  • atresia of ileum NOS
  • ileal atresia
  • ileum atresia
  • Congenital stricture of ileum

Inclusions

  • Congenital absence of small intestine
  • Congenital stenosis of small intestine

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB15.0 – Meckel diverticulum
  • LB15.2 – Congenital short bowel
  • LB15.3 – Congenital diverticulitis of small intestine
  • LB15.4 – Congenital diverticulosis of small intestine
  • LB15.5 – Congenital diverticulum of small intestine
  • LB15.Y – Other specified structural developmental anomalies of small intestine
  • LB15.Z – Structural developmental anomalies of small intestine, unspecified

Foundation entity

Atresia of small intestine – http://id.who.int/icd/entity/1949256262

Allowed postcoordination axes

Part of: LB15: Structural developmental anomalies of small intestine › 20: Developmental anomalies