LB16.3

ICD-11 MMS 2026-01

Congenital hypoganglionosis of large intestine

Description

The number and size of ganglion cells are small at birth. The size of ganglion cells tends to increase over time, but because their numbers do not increase the symptoms of dysmotility do not improve. Source: http://www.ncbi.nlm.nih.gov/pubmed/17161202

Index terms

  • Congenital hypoganglionosis of large intestine

Excludes

  • DB32.3 – Acquired hypoganglionosis of large intestine

Exclusions from above levels

  • LB17.2 – Persistent cloaca
  • LB17.Y – Congenital atresia of rectum
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB16.0 – Congenital absence, atresia or stenosis of large intestine
  • LB16.1 – Hirschsprung disease
  • LB16.2 – Immature ganglionosis of large intestine
  • LB16.Y – Other specified structural developmental anomalies of large intestine
  • LB16.Z – Structural developmental anomalies of large intestine, unspecified

Foundation entity

Congenital hypoganglionosis of large intestine – http://id.who.int/icd/entity/172127371

Allowed postcoordination axes

Part of: LB16: Structural developmental anomalies of large intestine › 20: Developmental anomalies