LB20.21

ICD-11 MMS 2026-01

Biliary atresia

Description

Biliary atresia is a rare disease characterised by an inflammatory biliary obstruction of unknown origin that presents in the neonatal period. It is the most frequent surgical cause of cholestatic jaundice in this age group. Untreated, this condition leads to cirrhosis and death within the first years of life.

Index terms

  • Biliary atresia
  • Atresia of bile ducts
  • BA - [biliary atresia]
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  • atresia of common duct
  • bile duct atresia
  • bile ductal atresia
  • biliary duct atresia
  • congenital bile duct atresia
  • congenital biliary atresia
  • cystic duct atresia
  • impervious bile duct
  • Extrahepatic biliary atresia
  • EHBA - [extrahepatic biliary atresia]
  • congenital atresia of extrahepatic bile duct
  • Intrahepatic biliary atresia
  • congenital hepatic ductal obstruction

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB20.20 – Choledochal cyst
  • LB20.22 – Congenital stenosis or stricture of bile ducts
  • LB20.23 – Structural developmental anomalies of cystic duct
  • LB20.24 – Accessory bile duct
  • LB20.2Y – Other specified structural developmental anomalies of bile ducts
  • LB20.2Z – Structural developmental anomalies of bile ducts, unspecified

Foundation entity

Biliary atresia – http://id.who.int/icd/entity/645741117

Part of: LB20.2: Structural developmental anomalies of bile ducts › LB20: Structural developmental anomalies of gallbladder, bile ducts or liver › 20: Developmental anomalies