LB22.0

ICD-11 MMS 2026-01

Congenital asplenia

Description

A condition caused by failure of the spleen to develop during the antenatal period. This condition may present with pneumococcal sepsis. Confirmation is through verification of no spleen by imaging.

Index terms

  • Congenital asplenia
  • Aplasia of spleen
  • Congenital absence of spleen
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  • Congenital absent spleen
  • Congenital aplasia of spleen
  • Congenital splenic absence
  • Spleen agenesis

Exclusions from above levels

  • LA8Y – isomerism of atrial appendages (with asplenia or polysplenia)
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB22.1 – Polysplenia
  • LB22.2 – Ectopic spleen
  • LB22.Y – Other specified structural developmental anomalies of spleen
  • LB22.Z – Structural developmental anomalies of spleen, unspecified

Foundation entity

Congenital asplenia – http://id.who.int/icd/entity/605819742

Part of: LB22: Structural developmental anomalies of spleen › 20: Developmental anomalies