LB40.0

ICD-11 MMS 2026-01

Absence of vulva

Description

This is a birth defect or congenital abnormality of the female genitourinary system that manifests itself in the absence of the vulva.

Index terms

  • Absence of vulva

Exclusions from above levels

  • LD2A – Disorders of sex development leading to sexual ambiguity
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB40.1 – Embryonic cyst of vulva
  • LB40.2 – Fusion of labia
  • LB40.Y – Other specified structural developmental anomalies of vulva
  • LB40.Z – Structural developmental anomalies of vulva, unspecified

Foundation entity

Absence of vulva – http://id.who.int/icd/entity/71592656

Part of: LB40: Structural developmental anomalies of vulva › 20: Developmental anomalies