LB44.2

ICD-11 MMS 2026-01

Unicornuate uterus

Description

A uterine malformation where the uterus is formed from one only of the paired Müllerian ducts while the other Müllerian duct does not develop or develops only in a rudimentary fashion.

Index terms

  • Unicornuate uterus
  • Uterus unicornis
  • Uterus unilateralis
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  • Uterus with only one functioning horn
  • Pseudo-unicornuate uterus
  • Incomplete unilateral aplasia of the Müllerian duct
  • Unicornuate uterus with rudimentary horn
  • Uterus pseudo-unicornis
  • True unicornuate uterus
  • Complete unilateral aplasia of the Müllerian duct
  • Congenital absence of one uterine horn
  • Single-horned uterus
  • True uterus unicornis
  • Unicornuate uterus without rudimentary horn

Exclusions from above levels

  • LD2A – Disorders of sex development leading to sexual ambiguity
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB44.0 – Agenesis or aplasia of uterine body
  • LB44.1 – Hypoplasia of uterus
  • LB44.3 – Bicornuate uterus
  • LB44.4 – Septate uterus
  • LB44.5 – Congenital fistulae between uterus and digestive and urinary tracts
  • LB44.6 – Uterovaginal malformation due to diethylstilbestrol syndrome
  • LB44.Y – Other specified structural developmental anomalies of uterus, except cervix
  • LB44.Z – Structural developmental anomalies of uterus, except cervix, unspecified

Foundation entity

Unicornuate uterus – http://id.who.int/icd/entity/1726108634

Part of: LB44: Structural developmental anomalies of uterus, except cervix › 20: Developmental anomalies