LB51

ICD-11 MMS 2026-01

Anorchia or microorchidia

Description

A disorder affecting males, caused by an abnormality occurring in sex development during the antenatal period. This disorder is characterised by individuals who are born with absence of the testes, or with testes that are deficient in size and function. Confirmation is by physical examination, identification of low testosterone levels but elevated follicle stimulating hormone and luteinizing hormone levels in a blood sample, or imaging.

Index terms

  • Anorchia or microorchidia
  • Absence or aplasia of testis, unilateral
  • absence or aplasia of testis
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  • aplasia of testicle
  • congenital absence of testis
  • congenital absence of testis, unilateral
  • congenital absent testicle
  • congenital aplasia of testicle
  • congenital aplasia of testis
  • monorchidism
  • monorchism
  • testis absence
  • Absence or aplasia of testis, bilateral
  • anorchia
  • anorchidism
  • anorchism
  • bilateral congenital aplasia of testicles
  • congenital absence of both testes
  • male agonadism

Exclusions from above levels

  • LD2A – Disorders of sex development leading to sexual ambiguity
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Foundation children elsewhere

  • LD2A.2 – Testicular agenesis

Sibling codes

  • LB50 – Micropenis or penis agenesis
  • LB52 – Cryptorchidism
  • LB53 – Hypospadias
  • LB54 – Congenital chordee
  • LB55 – Epispadias
  • LB56 – Bifid scrotum
  • LB57 – Agenesis of vas deferens
  • LB58 – Polyorchidism
  • LB59 – Hypoplasia of testis or scrotum
  • LB5Y – Other specified structural developmental anomalies of the male genital system
  • LB5Z – Structural developmental anomalies of the male genital system, unspecified

Foundation entity

Anorchia or microorchidia – http://id.who.int/icd/entity/997805288

Allowed postcoordination axes

Part of: 20: Developmental anomalies