LC02

ICD-11 MMS 2026-01

Complex epidermal hamartoma

Description

Hamartomatous malformation composed of elements deriving from several components of the developing epidermis and epidermal appendages.

Index terms

  • Complex epidermal hamartoma
  • Porokeratotic eccrine ostial and dermal duct naevus
  • Pigmented hairy epidermal naevus
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  • Becker melanosis
  • Becker naevus
  • Pilar smooth muscle hamartoma
  • Arrector pili hamartoma
  • Congenital pilar and smooth muscle naevus
  • Organoid naevus
  • Naevus sebaceus of Jadassohn
  • Sebaceous naevus
  • Epidermal naevus syndrome

Exclusions from above levels

  • 5C58.12 – Congenital erythropoietic porphyria
  • 5C64.20 – Acrodermatitis enteropathica
  • EG63 – pilonidal cyst or sinus
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LC00 – Keratinocytic epidermal hamartoma
  • LC01 – Pilosebaceous hamartoma
  • LC0Y – Other specified developmental hamartomata of the epidermis and epidermal appendages

Foundation entity

Complex epidermal hamartoma – http://id.who.int/icd/entity/923306251

Part of: 20: Developmental anomalies