LC10

ICD-11 MMS 2026-01

Dermal melanocytosis

Description

The presence at birth of functional melanocytes within the dermis. Most commonly this is as a result of incomplete migration of melanocytes to the epidermis as in lumbosacral dermal melanocytosis (Mongolian spot). Less commonly it is due to circumscribed hamartomatous proliferation of melanocytes in the dermis (e.g. Naevus of Ota).

Index terms

  • Dermal melanocytosis
  • Lumbosacral dermal melanocytosis
  • Blue spot
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  • Mongolian spot
  • Naevus of Ota
  • Oculodermal melanocytosis
  • Naevus of Ito
  • Dermal melanocyte hamartoma

Exclusions from above levels

  • 5C58.12 – Congenital erythropoietic porphyria
  • 5C64.20 – Acrodermatitis enteropathica
  • EG63 – pilonidal cyst or sinus
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LC1Y – Other specified developmental anomalies of skin pigmentation

Foundation entity

Dermal melanocytosis – http://id.who.int/icd/entity/1628237102

Part of: 20: Developmental anomalies