LC50.1

ICD-11 MMS 2026-01

Port-wine stain

Description

A port-wine stain is defined as a macular telangiectatic area of skin which is present at birth and does not spontaneously involute. Port-wine stains may be localised or extensive and they are often associated with an underlying disorder.

Index terms

  • Port-wine stain
  • Naevus flammeus

Exclusions from above levels

  • 5C58.12 – Congenital erythropoietic porphyria
  • 5C64.20 – Acrodermatitis enteropathica
  • EG63 – pilonidal cyst or sinus
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LC50.0 – Salmon patch
  • LC50.Y – Other specified developmental capillary vascular malformations of the skin

Foundation entity

Port-wine stain – http://id.who.int/icd/entity/2023437459

Allowed postcoordination axes

Part of: LC50: Developmental capillary vascular malformations of the skin › 20: Developmental anomalies