LC51

ICD-11 MMS 2026-01

Developmental venous malformations involving the skin

Description

Certain genetically-determined syndromes presenting with venous anomalies in the skin

Index terms

  • Developmental venous malformations involving the skin
  • Blue rubber bleb naevus syndrome
  • Bean syndrome (MIM 112200)
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  • Mucocutaneous venous malformations
  • Glomuvenous malformation
  • Bockenheimer syndrome
  • Congenital diffuse phlebectasia

Exclusions from above levels

  • 5C58.12 – Congenital erythropoietic porphyria
  • 5C64.20 – Acrodermatitis enteropathica
  • EG63 – pilonidal cyst or sinus
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LC50 – Developmental capillary vascular malformations of the skin
  • LC52 – Complex or combined developmental vascular malformations involving the skin
  • LC5Y – Other specified developmental anomalies of cutaneous vasculature
  • LC5Z – Developmental anomalies of cutaneous vasculature, unspecified

Foundation entity

Developmental venous malformations involving the skin – http://id.who.int/icd/entity/329960238

Allowed postcoordination axes

Part of: 20: Developmental anomalies