LC60

ICD-11 MMS 2026-01

Aplasia cutis congenita

Description

Congenital absence of skin. The commonest form presents as a defect limited to the scalp. It is also a component of a number of genetic syndromes.

Index terms

  • Aplasia cutis congenita
  • Syndromic aplasia cutis congenita
  • Aplasia cutis congenita due to adverse intrauterine events
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  • Aplasia cutis congenita secondary to adverse intrauterine events
  • Aplasia cutis congenita of limbs
  • Recessive aplasia cutis congenita of limbs
  • Aplasia cutis congenita of scalp

Exclusions from above levels

  • 5C58.12 – Congenital erythropoietic porphyria
  • 5C64.20 – Acrodermatitis enteropathica
  • EG63 – pilonidal cyst or sinus
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Foundation entity

Aplasia cutis congenita – http://id.who.int/icd/entity/350175828

Allowed postcoordination axes

Part of: 20: Developmental anomalies