Cronkhite-Canada syndrome

Description

Cronkhite-Canada syndrome (CCS) is a sporadically occurring, noninherited disorder of generalised gastrointestinal polyps (hamartomas), cutaneous pigmentation, alopecia, and onychodystrophy. The possibility of progression to cancer is considered to be low. Chronic diarrhea and protein-losing enteropathy are often observed.

Index terms

Cronkhite-Canada syndrome

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LD27.00 – Incontinentia pigmenti
LD27.02 – Hypohidrotic ectodermal dysplasia
LD27.03 – Hidrotic ectodermal dysplasia, Clouston type
LD27.0Y – Other specified ectodermal dysplasia syndromes
LD27.0Z – Ectodermal dysplasia syndrome, unspecified

Foundation entity

Cronkhite-Canada syndrome – http://id.who.int/icd/entity/79007466

Part of: LD27.0: Ectodermal dysplasia syndromes › LD27: Syndromes with skin or mucosal anomalies as a major feature › 20: Developmental anomalies