LD2H.1

ICD-11 MMS 2026-01

Neuropathy with hearing impairment

Description

Neuropathy with hearing impairment is characterised by the association of sensorineural hearing impairment and peripheral demyelinating and predominantly sensory neuropathy.

Index terms

  • Neuropathy with hearing impairment

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LD2H.0 – Fraser syndrome
  • LD2H.2 – Progressive deafness with stapes fixation
  • LD2H.3 – Waardenburg-Shah syndrome
  • LD2H.4 – Usher syndrome
  • LD2H.Y – Other specified syndromic genetic deafness
  • LD2H.Z – Syndromic genetic deafness, unspecified

Foundation entity

Neuropathy with hearing impairment – http://id.who.int/icd/entity/129297527

Part of: LD2H: Syndromic genetic deafness › 20: Developmental anomalies