XH1ZH1

ICD-11 MMS 2026-01

Pineoblastoma

Description

Pineoblastomas are a rare, malignant type of supratentorial primitive neuroectodermal tumour, found mainly in children (less than 10% of cases are reported in adults), located in the pineal region of the brain but that can metastasize along the neuroaxis. As they are the most aggressive of the pineal parenchymal tumours, they are usually associated with a poor prognosis.

Index terms

  • Pineoblastoma

Sibling codes

  • XH0FH0 – Askin tumour
  • XH17D8 – Chondroid chordoma
  • XH1S48 – Pineal parenchymal tumour of intermediate differentiation
  • XH2S71 – Mixed pineal tumour
  • XH3D20 – Transitional pineal tumour
  • XH6P76 – Peripheral primitive neuroectodermal tumour
  • XH7303 – Dedifferentiated chordoma
  • XH7K24 – Neuroectodermal tumour, NOS
  • XH8KJ8 – Ewing sarcoma
  • XH9GH0 – Chordoma, NOS

Foundation entity

Pineoblastoma – http://id.who.int/icd/entity/1679690951

Part of: X: Extension Codes