XH7E62

ICD-11 MMS 2026-01

Solitary fibrous tumour, NOS

Description

Solitary fibrous tumour (SFT) is a fibroblastic tumour characterized by a prominent, branching, thin-walled, dilated (staghorn) vasculature and NAB2-STAT6 gene rearrangement. SFTs affect men and women equally and are most common in adults, with a peak incidence between 40 and 70 years.

Index terms

  • Solitary fibrous tumour, NOS
  • SFT - [solitary fibrous tumour]
  • haemangiopericytoma
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  • localised fibrous tumour
  • Lipomatous solitary fibrous tumour
  • Giant cell–rich solitary fibrous tumour

Sibling codes

  • XH0TA8 – Atypical myxoinflammatory fibroblastic tumour
  • XH13Z3 – Aggressive fibromatosis
  • XH1EH1 – Solitary fibrous tumour/Haemangiopericytoma, grade 2
  • XH1N00 – Myofibromatosis
  • XH1RM7 – Atypical fibrous histiocytoma
  • XH2D15 – Myxoinflammatory fibroblastic sarcoma
  • XH4GL1 – Plexiform fibrohistiocytic tumour
  • XH4QZ8 – Dermatofibrosarcoma protuberans, NOS
  • XH5CT4 – Pigmented dermatofibrosarcoma protuberans
  • XH5MH2 – Congenital generalised fibromatosis
  • XH6116 – Abdominal fibromatosis
  • XH66Z0 – Myofibroblastic tumour, NOS
  • XH6YK5 – Desmoplastic fibroma
  • XH7050 – Haemangiopericytic meningioma
  • XH75J5 – Palmar/plantar type fibromatosis
  • XH85R1 – Myofibroblastic tumour, peribronchial
  • XH9362 – Angiomatoid fibrous histiocytoma
  • XH9526 – Haemosiderotic fibrolipomatous tumour
  • XH9AV8 – Giant cell fibroblastoma
  • XH9HH5 – Cellular fibroma

Foundation entity

Solitary fibrous tumour, NOS – http://id.who.int/icd/entity/1652009742

Part of: X: Extension Codes